Anesthetic management of a patient with Huntington's chorea -A case report-
نویسندگان
چکیده
Huntington's chorea is a rare hereditary disorder of the nervous system. It is inherited as an autosomal dominant disorder and is characterized by progressive chorea, dementia and psychiatric disturbances. The best anesthetic technique is yet to be established for these patients with increased risk of aspiration due to involvement of pharyngeal muscles and an exaggerated response to sodium thiopental and succinylcholine. The primary goal in general anesthesia for these patients is to provide airway protection and a rapid and safe recovery. We report the anesthetic management of a 51-year-old patient with Huntington's chorea admitted for an emergency operation.
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اداره بیهوشی در بیمار مبتلا به کره هانتینگتون کاندید عمل جراحی کوله سیستکتومی
Aims and background: Huntington’s chorea )HC( is a rare, autosomal, dominant hereditary disorder of the nervous system. This disease is characterized by progressive chorea movement, dementia and psychiatric disorders. In these patients, an abnormal response to many anesthetic drugs has been observed. The primary goal of general anesthesia in these patients is airway protection and a fast and ...
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